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Kawasakis sjukdom

Senast uppdaterad: Senast reviderad:
Sakkunnig:


Definition:
Akut, febril självbegränsande vaskulit av okänd orsak som oftast drabbas barn under 5 år.
Förekomst:
I Sverige beräknas incidensen till 2,9 per 100 000 barn under 16 år och 6,2 per 100 000 barn under 5 år, det vill säga sammantaget cirka 50 barn per år
Symtom:
Symtom är feber i minst fem dagar samt fyra av följande fem kliniska fynd.
Kliniska fynd:
Fyra av följande fem fynd måste konstateras för diagnosen: konjuktivit, makulopapulöst utslag, ensidigt förstorade cervikala lymfkörtlar, slemhinneförändringar på läppar och i munhåla, rodnad och ödem i händer och fotsulor. 
Diagnostik:
Labbprover är inte diagnostiska, men ofta ses leukocytos, trombocytos, förhöjd SR och CRP. 
Behandling:
Immunoglobulin ges intravenöst i kombination med acetylsalicylsyra. Detta sker på sjukhus.
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  • Athena Adeli, legitimerad läkare, Karolinska Institutet

Tidigare sakkunniga

  • Bengt Granström, överläkare, Barn-och ungdomsmedicinska kliniken, Skånes universitetssjukhus